The hémochromatose is a recessive autosomic disease being characterized by an iron overload in the organization reaching several bodies, mainly the liver, the pancreas, the heart and the pituitary gland. In the long run, these ferric deposits generate anatomical and functional lesions irréversibles.

One distinguishes:

• the primitive hémochromatose of genetic cause of which there exist several types in connection with gene reached. The table below summarizes the various types of hémochromatose primitive:

• the secondary hémochromatose related to an endogenous ferric overload (hemopathy or thalassaemia) or exogenic (transfusion with repetition).

Physiopathology

1.Metabolism of iron

2.Metabolism of iron in the hémochromatose

3.Surcharges secondary